Surgical treatment of pulmonary sequestration in children

Pulmonary sequestration is a complex malformation of the lungs, which based on violation development their bronchopulmonary and vascular components. The multifactorial nature morphological functional disorders clinically manifested by respiratory distress syndrome heart failure with threat critical outcome for newborn child, despite sufficient system as whole. Purpose - optimization diagnosis treatment lung in children study clinical diagnostic data, well results surgical treatment. Materials methods. included 18 patients aged from 8 days to years, including newborns 6, 1 12 months 5, 3 years 3, 7 9 2 15 2. Median age was 4.5 months. Research methods evaluation symptoms, chest X-ray, contrast-enhanced CT, angiography. Prenatal carried out using ultrasonography fetal MRI. In all cases, open used. Results. Intrapulmonary diagnosed 13 (72.2%) patients, extrapulmonary 5 (27.8%), p=0.082. Left-sided localization 11 (61.1%) right-sided (38.9%) р=0.3. Associated malformations had (50%) patients: polycystic (n=4) or hypoplasia (n=2) lung, diaphragmatic hernia (n=3), pericardial defect (n=1), thoracic dystopia kidney (n=2), Waardenburg ventricular septal innominate artery tracheal compression (n=1). Symptomatic course noted (83.3%) asymptomatic (16.7%) cases (p=0.021). Main symptoms were follows: pulmonary bleeding, hemophthisis, hemodynamic disorders, signs inflammation. Lobectomy (n=8), atypical segmental resection transection aberrant vessels (n=1) performed intrapulmonary sequestration, sequestrectomy sequestration. associated simultaneous plasty performed, non-free flap PTFE patch case trachea, aortopexy 17 (94.4%) positive result noted. Postoperative complications (intrathoracic bleeding) lethality observed (5.6%) case. Patients examined long-term period 30 after surgery. Conclusions. Surgical correction appropriate made, mainly neonatal period. Given complexity pathology, especially presence malformations, expediency early period, thoracotomy access should be preferred safer sequential division arterial then venous vessels, lobectomy, depending peculiarities sequester. defects requires correction. hernia, autopericardial plastics synthetic are an alternative simple suturing. research accordance principles Helsinki Declaration. protocol approved Local Ethics Committee participating institution. informed consent patient obtained conducting studies. No conflict interests declared authors. Keywords: congenital treatment, children.